Surgical treatment of Hirschsprung’s disease at the National Children’s .. Enfermedad de Hirschprung. Fantobal-Rojas A. Constipación crónica en el niño. La enfermedad de Hirschsprung es un trastorno congénito infrecuente (afecta aproximadamente a 1 de cada recién nacidos en EE. UU.) que provoca. El estreñimiento se debe diferenciar de la enfermedad de Hirschsprung y de alteraciones anatómicas y metabólicas. La evaluación clínica incluye una historia.

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The other two children were able to maintain regular bowel habits with the use of regular laxatives 1 and enemas 1. The challenge for healthcare providers throughout the islands of the Caribbean, especially in the smaller islands, is to identify children who do not have primary constipation, but are constipated from treatable underlying medical or surgical conditions, for example Hirschsprung’s disease HD.


Findings are enfermedwd those of a bowel obstruction. Transanal endorectal pull-through for Hirschsprung’s disease. The 11 children excluded from long-term follow-up included two with total colonic HD – one of whom had definitive surgery elsewhere, three who were lost to follow-up, one child whose parents declined to take part in the study, one child awaiting definitive surgery, one child who had a stoma at the time of study and three who did not have a Martin’s modified Duhamel procedure as definitive surgery for HD.


It is then imperative niks these children be referred as early as possible for specialist care, and once referred appropriately managed. Hirschsprung disease in the newborn. Interestingly, it is almost never seen in premature infants. Six of the children presenting in the neonatal period, did so within 48 hours of life with intestinal obstruction vomiting and abdominal distension and had laparotomy.

Medicina12 1 To assess the surgical outcome of patients hirschsprhng Hirschsprung’s disease HD who were treated in Barbados, establish referral patterns and identify factors which hirschspdung lead to better management. In short segment disease, there is a significant predilection for males M: Hence, functional obstruction develops as a result of a spasm in the denervated colon.

About Blog Go ad-free. Hirschsprung disease is characterised by aganglionosis absence of ganglion cells in the distal colon and rectum.

Accllracy of the hariulll enema examination. The affected segment is of small caliber with proximal dilatation. A very small number may present in the adult population 1. For example, awareness of HD will improve with increased educational and training opportunities created both locally and abroad.

Support Radiopaedia and see fewer ads. Semin Pediatr Surg ; Veinte eran varones y siete hembras. Long term outcome was assessed by the use of a simple questionnaire completed by the junior author MVV after personal or telephone contact with patients, their parents or guardians or the hjrschsprung physician.

While transportation and poor communication systems may indeed be a challenge for the Caribbean, especially in the presence of multiple small islands, a number of factors make routine use of the primary pull-through procedure inappropriate for the Caribbean, if not impossible. Recuperado a partir de https: Synonyms or Alternate Spellings: Over a year period, between July and Juneenfermedas children were identified with Hirschsprung’s disease HDincluding twenty males and enn females – [male: Hirschsprung’s disease in Barbados a year review.


J Pediatr Surg ; 8: It is a known fact that the clinical features of NEC – foul-smelling, explosive diarrhoea, often bloody in nature, abdominal distention, hypovolaemic shock, vomiting, fever and lethargy may mimic ebfermedad of Hirschsprung’s enterocolitis. EnBretano, informa casos similares.

[Hirschsprung’s disease: the immunohistochemistry as ancillary method for the diagnosis.]

For this reason, the senior author SUJ prefers not to perform primary pull-through procedures. Diagnostic Imaging in children with acute chest and abdominal disorders. The frequency of HD at young edges is higher on men, but as the edge grows, it occurs more in women.

Ineluding sixty-seven consecutive Endorectal Pullthrough procedures. A carefully performed contrast enema is indispensable in both the diagnosis of Hirschsprung disease but also in assessing the length of involvement. Long-term follow-up in patients.